Processing of CFTR bearing the P574H mutation differs from wild-type and deltaF508-CFTR

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Articles by Ostedgaard, L. S.

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				L. S. Ostedgaard, C. S. Rogers, Q. Dong, C. O. Randak, D. W. Vermeer, T. Rokhlina, P. H. Karp, and M. J. Welsh Processing and function of CFTR-{Delta}F508 are species-dependent PNAS, September 25, 2007; 104(39): 15370 - 15375. [Abstract] [Full Text] [PDF]

				S. L. Farmen, P. H. Karp, P. Ng, D. J. Palmer, D. R. Koehler, J. Hu, A. L. Beaudet, J. Zabner, and M. J. Welsh Gene transfer of CFTR to airway epithelia: low levels of expression are sufficient to correct Cl- transport and overexpression can generate basolateral CFTR Am J Physiol Lung Cell Mol Physiol, December 1, 2005; 289(6): L1123 - L1130. [Abstract] [Full Text] [PDF]

				A. L. Berger, C. O. Randak, L. S. Ostedgaard, P. H. Karp, D. W. Vermeer, and M. J. Welsh Curcumin Stimulates Cystic Fibrosis Transmembrane Conductance Regulator Cl- Channel Activity J. Biol. Chem., February 18, 2005; 280(7): 5221 - 5226. [Abstract] [Full Text] [PDF]

				X. Wang, J. Matteson, Y. An, B. Moyer, J.-S. Yoo, S. Bannykh, I. A. Wilson, J. R. Riordan, and W. E. Balch COPII-dependent export of cystic fibrosis transmembrane conductance regulator from the ER uses a di-acidic exit code J. Cell Biol., October 11, 2004; 167(1): 65 - 74. [Abstract] [Full Text] [PDF]

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				L. S. Ostedgaard, C. Randak, T. Rokhlina, P. Karp, D. Vermeer, K. J. Ashbourne Excoffon, and M. J. Welsh Effects of C-terminal deletions on cystic fibrosis transmembrane conductance regulator function in cystic fibrosis airway epithelia PNAS, February 18, 2003; 100(4): 1937 - 1942. [Abstract] [Full Text] [PDF]

				J.-S. Yoo, B. D. Moyer, S. Bannykh, H.-M. Yoo, J. R. Riordan, and W. E. Balch Non-conventional Trafficking of the Cystic Fibrosis Transmembrane Conductance Regulator through the Early Secretory Pathway J. Biol. Chem., March 22, 2002; 277(13): 11401 - 11409. [Abstract] [Full Text] [PDF]

				L. S. Ostedgaard, J. Zabner, D. W. Vermeer, T. Rokhlina, P. H. Karp, A. A. Stecenko, C. Randak, and M. J. Welsh CFTR with a partially deleted R domain corrects the cystic fibrosis chloride transport defect in human airway epithelia in vitro and in mouse nasal mucosa in vivo PNAS, February 14, 2002; (2002) 261714599. [Abstract] [Full Text] [PDF]

				M. Van Oene, G. L. Lukacs, and J. M. Rommens Cystic Fibrosis Mutations Lead to Carboxyl-terminal Fragments That Highlight an Early Biogenesis Step of the Cystic Fibrosis Transmembrane Conductance Regulator J. Biol. Chem., June 23, 2000; 275(26): 19577 - 19584. [Abstract] [Full Text] [PDF]